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Abstract

Techniques in Neurosurgery & Neurology

Myxofibrosarcoma of Base of Skull in Paediatric Age Group: A Case Report

  • Open or Close Zafar Ahmed Sheikh*

    Mahatma Gandhi Memorial Medical College, India

    *Corresponding author: Zafar Ahmed Sheikh, Mahatma Gandhi Memorial Medical College, G1 Kasturi Apts, 12 Shankar Nagar, Saket Extension, Indore-452018, Madhya Pradesh, India

Submission: March 08, 2018; Published: August 31, 2018

DOI: 10.31031/TNN.2018.02.000530

ISSN 2637-7748
Volume2 Issue1

Abstract

Myxofibrosarcoma is a common sarcoma affecting extremities of elderly age group. It rarely affects the younger age group and the head neck reg ion. It exhibits an infiltrative growth pattern and has a high local recurrence rate. We report a 14 year old patient with a myxofibrosarcoma of base of skull. The patient’s age and clinical presentation favored a bed side diagnosis of a dermoid cyst or langerhans cell histiocytosis, radiology was suggestive of an intraosseous hemangioma and surgical pathology favored a low grade Osteosarcoma. However, tissue immunohistochemistry clinched the diagnosis of a Myxofibrosarcoma. He underwent a near total excision with adjuvant radiotherapy and remains recurrence free at one and a half year follow up. Tissue immuno chemistry played a pivotal role in the management of our patient. We have attempted to bring forward the pertinent neurosurgical issues related to the management of this common soft tissue sarcoma which is rarely encountered by Neurosurgeons.

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