Abstract

EDS (Ehlers-Danlos syndrome) is a group of connective tissue disorders that has a common genotypic defect, but heterogeneous phenotypic presentations. This case report presents a successful pregnancy outcome in a woman diagnosed with an unknown type of Ehlers-Danlos syndrome. The various types of EDS can result in either no complication to severe complications with pregnancy and delivery. Several studies and a review of the literature suggest that, generally in pregnant women with EDS, maternal and neonatal outcomes are favorable. However, in EDS type IV, pregnancy can be associated with serious maternal complications. Therefore, there is a challenging situation for obstetrician and obstetrical management should be individualized. This study discusses the obstetric management of a patient with EDS unknown type and compares it to other studies in the literature.

Keywords:D Ehlers-Danlos syndrome; Pregnancy outcome; Delivery management