Abstract

Seckel syndrome or Microcephalic primordial dwarfism is a rare, autosomal recessive, congenital disorder characterized by severe intrauterine and postnatal growth retardation, microcephaly, mental retardation, and typical facial appearance with beaklike protrusion of the midface. Dental abnormalities include enamel hypoplasia, hypodontia, microdontia, taurodontic root morphology and a high-arched palate. This is a case report of implant supported dental prosthesis in a 19-year-old male with Seckel syndrome. Two implant were placed in the area of #12 and 22. Three months’ post implantation, the site was examined to ensure the osseointegration. A four-unit implant supported screw-retained porcelain fused to metal bridge was attached. Occlusion was checked and oral hygiene instructions were given to the mother. The case was followed up for three years. The osseointegration was excellent with no untoward findings. To the best of our knowledge, this is the first report of implant supported fixed partial denture in Seckel Syndrome patient.