Consultant- Mittal Ortho Centre, 97 New Lal Bagh Colony, Patiala (Punjab) 147001, INDIA Emeritus Professor Orthopaedics, GOMCO Patiala
*Corresponding author: Mittal RL, Emeritus Professor, Orthopaedic Department, Government Medical College Patiala, India
Submission: May 12, 2020;Published: May 26, 2020
ISSN: 2576-8875 Volume7 Issue1
Background: Author published a comprehensive research article on trimorphic extreme clubfoot deformities , offering, all-inclusive, triple/ quadruple surgical techniques, a far reaching solution, which received tremendous Global attention. This generic name (trimorphic extreme clubfoot deformities) was given, by the author, to scores of brand names in literature, reporting 95% failures post-surgeries with contemporary techniques. “Each Clubfoot Is Different” an important discovery therein, was prominently considered, for grading of results, rather than the prevalent assessment criteria of Pirani’s or Demiglio’s etc. Additional thoughts on this were recorded in author’s invited BOOK on CLUBFOOT, published by Taylor and Francis (Informa group London U.K), ISBN: 9781138083738, released on 29th November, 2018 IOACON at Coimbatore (India). Author also performed, here, a Hat Trick, in clubfoot research, getting third best IOA original research award i.e. Diamond jubilee also; Golden and Silver awards bagged earlier in 2013 and 1988 respectively. During last about two years, as per its name, this research made significant headway with countless new features. Therefore, this has been christened as “Mother of all clubfoot discoveries/inventions”, with its deep seated roots and incredible unity in diversity in its All-inclusive, corrective, 4-in-1, surgical concept. Being so and with its unending future research potential, it needs to be free from the lockdown of Journal and BOOK, to spread awareness for the welfare of poor clubfoot community in LMICs, having more than 80% global population.
Methods: Recently concieved new features are: Firstly, formulating a comprehensive classification under numerous broad headings: Limitless variations in deformity start at birth; get modified with age, patient’s weight, weight bearing, physical activity, treatments, early/ delayed complications, radiological variations etc. Secondly, the landmark, revelation in Rediscovery of Octopus Clubfoot, DOI: 10.31031/OPROJ.2019.06.000627 and stamping its surgical correction as all-inclusive, branded, surgical concept; A Unity in Diversity. This was proved earlier by actually showcasing innumerable diverse deformities with gratifying results in author’s International Orthopaedics as well as BOOK publications. This has been further strengthened with more new cases in this article (Table 1). Thirdly, many newer surgical steps have been added in the surgical corrections of these cases in the appropriate section in this article.
Results and Conclusion: This MASTERSTROKE article, a GRASSROOTS DISCOVERY, needs to spread awareness for an impactful message, giving a far better deal to poor Clubfoot community of LMICs, at lesser cost, with longer, good looking, better functioning feet, on long term, without any bony fusion and improving the patient’s psycho-physico-socio-economics, helping indirectly their countries economy. The research in this entity is unending, each being different, therefore increasing awareness highly important. This will increase the demand for these surgeries and thereby a need for learning these comprehensive techniques through available internet channels and setting things going.
Keywords: Mother of clubfoot innovations; “Each clubfoot is different”; Extreme clubfoot deformities; Fusion 4-in-1 surgical concept; Octopus clubfoot rediscovered; Unity in diversity; Triple/ Quadruple surgical skin expansion; Cosmetic/Plastic surgery in clubfoot; Rozy feet
Abbreviations: AGMC: Arthrogryposis Multiplex Congenita; CCBs: Congenital Constriction Bands; CPC: Conjoint Posterior Capsule, DALYs: Disability Adjusted Life Years; DL: Dorsolateral; DOLAR: DOrso-Lateral Rotation; EQ: Equinus; FDP: Flexor Digitorumlongus; FHL: Flexor Halluces Longus; GBD: Global Burden of Disease; IOA: Indian Orthopaedic Association; IOACON: IOA Conference; IT: Intertarsal; ITC: Interosseoustalocalcanean; OA: Osteoarthritis; PMPDLR: Posteromedial Plantar Dorsal Lateral Release; TMT: Tarsometarsal
“Each Clubfoot is Different” is the Mother of all Clubfoot inventions/ discoveries. It is like a ROSARY of countless beads, unified by its, 4-in-1, surgical concept. Author published in 2018, an original research article , Doi.10.1007/s00264-017-3741-6, receiving tremendous positive Global response. This research had been carried out in trimorphic deformities (a new name), with its equally matchless, infallible, surgical solution. To recapitulate 2018 article briefly, clubfoot remained unsolved, in spite of vast literature, with high prevalence rate of 95% failures, in neglected deformities with scores of brand names and no acceptable surgical solution [2-4]. Author researched this grey area in, need based, three phases, clustering all such brand names as trimorphic extreme deformities (three hierarchic grades), with an aim to improve upon contemporary surgical techniques. Posteromedial 3D skin contractures, in increasing severity, were discovered as the reasons for universal failures, which were corrected by all-inclusive, innovative, graded, expansion of fascio-cutaneous chamber for increasingly severe/ rigid deformities.
First phase, in two stages, was the longest and continued for 25-30 years, including years of building a strong foundation of critical analysis of prevalent failures in literature. 1st stage was study of patho-anatomy, in 15 clubfeet of stillborn foetuses, published 1981 , discovering skin contracture as primary cause, reinforced by years of clinical observations. Second stage was a successful clinical study of 100, grade 1, extreme deformities, treated by DOrso Lateral Rotation skin flap (DOLAR technique - an acronym) 1987 .
Second phase continued for about 10-15 years, in grade 2 deformities in older children, requiring more skin expansion, adding Z-plasty also in Rotation flap, in the same incision, as 2-in-1 incision. This was named as DOLARZ technique .
Third phase, still continuing, in grade 3 deformities, are mostly adolescents/ adults, requiring even more skin expansion, adding VY-plasty also in the same incision, as 3-in-1 incision, named DOLARZ-E,. E means extended, because it is not only VY-plasty, but extended too many other skin procedures used and described later in surgical steps. For still more expansion, fourth plastic surgery procedure i.e. fillet flap was also added in same incision, as 4-in-1, for correcting World’s First, Octopus Clubfoot (a new name), published [1,8].
Third phase has been the most significant, opening floodgates with unending new research possibilities. An unbelievable revelation, Mother of all discoveries/ inventions, i.e. “Each Clubfoot is Different” also emerged in this phase. An equally incredible realization of their infallible, all-inclusive 4-in1 treatment protocol, also unfolded, which was stamped as a universal surgical concept, with an unparalleled Unity in Diversity. This firm assertion was a flashback on rediscovery of excellent correction in 2016 of Octopus Clubfoot , World’s First and most extreme Clubfoot deformity in 18 years old female. If this can be corrected, then any and every other must also be correctible this exotic patient had good media coverage: an interview by London UK media at Link: “dailymail.co.uk/health octopus clubfoot”, https://www.hindustantimes.com/punjab/girl-with-eight-toes”; and Asian Age “Indian teen born with deformed foot can finally wear shoes www.asianage.com/newsmakers/180617/indian-teen”, viral on Google search.
Evolution of 4-IN-1 Concept: This has been an evidence based research, since over 50 years. Firm evidence is derived from National and International plastic surgery literature [10-22] of cadaveric dissections, animal experiments and clinical experience. There is extensive vascular and lymphatic microcirculation, in the subfascial and suprafascial planes, with countless perforators arising from the deepest to most superficial planes. This was convincing enough for phased unification of the four plastic surgery procedures for MEGA skin expansion, as needed, in extreme deformities. One must remain outside in suprafascial plane, avoiding injury to perforators. Considering the site and size of gaps, distal based VY island flaps of various sizes, are designed in the same incision; in front, below or behind the medial malleolus. When old surgical scars are present, there may occasionally be marginal necrosis, without affecting the correction of deformity, due to extremely good vascular network of collaterals by perforators.
Each clubfoot is different
This is an evidence based new concept, mentioned briefly in SICOT Publication and with some more detail in author’s book. More differently innovative thoughts have been added during the last about two years. Each clubfoot is different with countless variables, even in the same patient with increasing age. With endless variations, it will be more appropriate to call it clubfoot disease:
Figure 1: New perspective of equinus EQ1 to EQ5 as 5 hierarchic grades of plantar-flexion shown as (G1 - G5), highly important from treatment point of view.
Figure 2: Each clubfoot is different- 1st, 3rd and 4th rows showing that each is different from the others at all ages and 2nd row shows Ponseti’s heel Cord tenotomies with varied under-corrections and relapses.
Figure 3: Showing varied surgical scars- adherent, extensive, ulcer, bow string, multiple etc.
Figure 4: Collage of various complications labelled below each picture.
Each deformity is a separate entity, requiring individual assessment and treatment planning, without a copy paste attitude.
There are scores of surgical steps needed to correct extreme deformities. The usual surgical steps needed in a virgin uncorrected deformity are summed up as an extensive PMPDLR. However, other steps, needed sometimes, are also described, details varying in the wider trimorphic domain.
For Grade 1, it is a dorsolateral Rotation skin flap (DOLAR) as a single procedure, or as 2-in-1 i.e. DOLAR + Z-plasty on the medial side in Grade 2, (one or more Zs). In grade 3, VY-plasty is added (3-in-1) and occasionally fillet flap can be added as 4-in-1  in any appropriate case. Many times decision has to be taken at the operation table itself. Besides the four plastic surgery procedures, many other skin procedures have been used, for correcting diverse rigid deformities, especially when old scars are excised and wound closure is not possible; these are: proximal relaxing incision, one or more lazy z or v to lengthen skin, Thiersch grafts for minor skin defects, double VY-plasties: either side by side or above and below, circular Z-plasties in CCBs in 4 sections; separate VY-plasties; a distal medial one to correct hallux varus, dorsal for hyperextended toes and plantar for hammer toes.
Muscles & tendons releases
Abductor hallucis, Steindler’s, tibialis posterior insertions; FHL & FDP at Henry’s knot releases, Z-lengthening of distal heel cord or proximal in case of distal scar, lengthening of tibialis anterior or extensor halluces longus in their contractures ; Ligaments/capsules: spring ligament, CPC, Kendrick’s TMT mobilization, ITC release, medial and plantar IT and TMT ligaments releases; Osseous: DL wedge resection from cuboid and if required, from cuneiforms, open wedge osteotomy of medial cuneiform with a bone graft from cuboid and talo-navicular reduction. Multiple K-wires fixations are done to maintain correction. Wound closure is done after manipulating the flaps to get maximum skin chamber enlargement. Details of all deeper releases of muscles, tendons, ligaments, capsules and bones can be read in author’s publications [1,6,8]. In under-corrected and relapsed cases with adherent scars of earlier surgeries, conventional surgery is not possible, due to dense adhesions and obscurity of deeper structures. However, besides excising the scars, the basic concept of PMPDLR remains the same, remaining close to bones, avoiding injury to neurovascular structures and achieving a good correction.
In diverse situations, our aim is to achieve the best possible correction without arthrodesis by innovative modifications, many times decided at the operation table. The rational concept of unified 3 and 4-in-1 skin expanding techniques will always make it possible, in spite of, EACH CLUBFOOT BEING DIFFERENT. This has been very well proved, in variety of cases in earlier publications [1,6,8] and many more recent ones in Table 1 in this article. Learning the techniques is not difficult form various publications of author and youtube videos at author’s channel “Patiala Clubfoot Foundation”. These are more cost effective than others and giving far better results, more satisfying to patients on long term. Immediate surgical operative costs are much less, besides the lifelong gain in psychophysico- socio-economics of the patients (Figure 5 & 6).
Table 1: Showing variety of cases, each different.
Abbreviations of Table 1: Adhesions (Adhes), Amputation (amp), Anterior capsulotomy ankle (ACA), Bilateral (BL), Calcaneum (Calc), Callosity numbers as superscript (Callos2), Circumferential (Circ), Child (C), Congenital amputation (Cong amp),Congenital Constriction bands (CCBs), Cock-up big toe (CUBT) Calcaneo-varus (CV), Dorsiflexors (DFs); Dorsolateral (DL), Equino-cavo-varus (ECV), Equinus1-5 (EQ1-5), Fasciocutaneous VY-Plasty Great Toe (FCVYGT); Fixed dorsiflexion deformity(FDFDef), Female (F), Follow up (FU), Flexion deformity (FD), Figure (Fig), Female (F), First (1st), Flexion deformity (FD), Flexor digitorum Brevis Tendon Release (FDBTR), Free Tendon Grafting (FTG), Flexor Hallucis Longus (FHL), Great toe (GT), Grade (Gr), Heel Cord adhesions (HC adhes); Heel Cord Tenotomies number shown as superscript (HCT2), Hallux varus (HV), Increased Inc), Intertarsal (IT), Left (Lt), Right (Rt), Metatarsals (MT), Male (M), Year (Y), Months (mths), Muscle power gr 0-5 dorsiflexors (DFs Zero), Operation (Op), Osteoarthritis Talonavicular joint (OATNJt), Plantar-flexion (PF), Postero-medial-dorsalplantar- lateral release (PMDPLR), Partial thickness skin graft, (PTSG), Ponseti casts (Pcasts), Patient (Pt), Proximal Relaxing Incisions (Prox.RI), Proximal Tendoachilles Lengthening Z-plasty (ProxTALZ); Relapse numbers shown by superscript (Relap2), Residual equinus (RE), Previous treatment Prev tt); Resection (resect), Relaxing incisions (RIs), Required Reqd), Surgery (Surg), satisfaction (satisfac); Serial number (S. No), Second (2nd), Talo-navicular (TN), Scars of number of earlier surgeries shown as superscript (Scars2), Tendoachilles (TA)Tibialis anterior Z-lengthening TibALZ); Tarso-metatarsal (TMT), Two stage surgergies (Surg2), X-ray Interosseous Relationship disturbed (X-IORD), Dorsolateral Wedge resection (DLWR), Year (Y), Z-plasty or ies (Z or Zs), Z Lengthening of Tendoachilles (ZTAL).
5(Table 1): Case-1(i-iv) HCT3 scars, scarred TA and corrected deformity; Case-2(v-ix) Stands lateral border, HCT1scar, irregular scar collagen, Prox ZTAL and correction; Case-3(x-xiv) HCT1, EQ3, scar TA, Prox ZTAL, corrected def and prints; Case-4(xv-xx) CCBs, HCT1, callos, scarred TA with gap below, Prox ZTAL, corrected def and healed callos; Case-6(xxi-xxv) HCT1 BL, EQ4, BL DOLARZ-E, Corrected Defs BL; Case-13(xxvi-xxxi) EQ4, Callos2, DOLARZ-E and 2 RIs with 3 split skin grafts patches, corrected def with all scars well healed.
6: Magnified views of case 13 table1, #-in-1 + 3 Thiersch grafts on relaxing incisions to Cover the raw areas and final healing, normally walking at 5 months follow up.4eview
Extreme clubfoot deformities have been a life time research area of author, pursued in three phases, since over 50 years. It can very well be compared with the story of famous Chinese bamboo tree, establishing strong root system for many years before it sprouts up . Similarly, this research took many years (about 15 to get firmly rooted and rationalized for execution, before the experimental and three phased (grade 1-3) clinical studies.
It has emerged, as a need based research, from highly prevalent under-corrections/ relapses of over 95%, in extreme deformities (a new generic name given by author), reported in literature with scores of confusing brand names of neglected deformities treated by contemporary surgical techniques, including the popular ones.
“Each Clubfoot is Different” is the SOUL of the research, a powerful Mother innovation, with potential for changing Global thinking about clubfoot. This was an afterthought in the third phase of this research, an unprecedented powerful Grassroots discovery, now a grown up tree with its umbrella of countless branches and leaves, each different, yet all connected with the roots. So are the countless, varied deformities getting unified in their all-inclusive surgical concept. This discovery, with potential for changing global thinking about clubfoot, emerged from highly prevalent under-corrections/relapses of over 95%, reported in literature, with scores of confusing names. The contemporary surgical techniques, including the popular ones: Ponseti’s and Illizarov’s, do not succeed in extreme deformities. Ponseti technique succeeds in mild and moderate deformities, if his guidelines of right age, type of deformity, casting technique, bracing and follow up are strictly followed,. Being labour intensive, these are neglected by care givers as well as recipients, with numerous pitfalls, reported by Ponseti himself in details in their own articles [5,6], in author’s book and many others. In spite of Ponseti’s advice against using in more rigid/ severe deformities, vast majority are still doing and failing. First eight cases in Table 1, in this article, are testimony to this assertion. Heel cord tenotomy does more harm than good. It leads to dull white irregular collagen in the gap with adhesions all round, with persisting under-corrected varus and later on relapses (Table 1, Figure 5; cases (1-4,6,15)). Bones grow, but scars do not and hence increasing relapses with age, emphatically asserted by Ponseti himself, and quoted by author .
Heterogeneous skin contractures, primary alone or with surgical scars, have always remained neglected, with imperative need for correction. The cramped cell-like room has to be enlarged in 3D, giving proper head and leg space to each occupant and accommodate all in orderly position. This became realty with the invention of triple or even quadruple surgical mega skin expanding incision, each in 3D, as FUSION 3 or 4-in-1. The four plastic surgery procedures of Rotation flap, Z-plasty, VY-plasty and Fillet flap are commonly used as single procedures. Author merged all four procedures into an unprecedented single incision for maximum fascio-cutaneous chamber expansion. It is abundantly, evidence based and time tested too. This was in three phases, as need based procedures, because, with spreading awareness, more and still more severe/rigid deformities presented for treatment, requiring increasing skin expansion. The extensive deeper soft tissue and osseous releases get reattached in the foot in the corrected position and stabilize. With increasing grade of deformity, they are used as single, 2-in-1, 3-in-1 or 4-in-1, without any bony fusion in vast majority, getting a longer, good looking, flexible and better functioning foot on long term than by other techniques. In still more rigid deformities, some other skin may also be used; as in case No. 13 Table 1, when wound closure was not possible 2 relaxing incisions were given and raw areas were covered with Thiersh grafts from adjacent part of lower leg with uneventful wound healing and patient normal at 5 months follow up (Figure 6. I-iii enlarged views)
After treating the world’s First, most rigid/ severest deformity, OCTOPUS CLUBFOOT in 2016, these surgical techniques, of Fusion 4-in-1, have now become an imprinted all-inclusive surgical concept, correcting any and every deformity. Learning this evidence based concept is not difficult for clubfoot enthusiasts. This surgical concept is like a Master Key opening all locks.
Working out the economics, WHO documents of 2004 and 2008 , on congenital anomalies including clubfoot, quote a very high loss of DALYs of 25.3-38.8 million globally. As regards GBD, congenital anomalies, including clubfoot, ranked as 17th cause of GBD. Feet are an organ of locomotion for daily living and earn livelihood. Extreme clubfooted, especially bilateral, will earn less or nothing, adding to GBD. These surgical techniques are not costlier than others. Global clubfoot community in LMICs, with over 80% population, is looking towards us expectantly for a better deal and giving them a full meal with lesser cost, rather than costlier half meal. They are not difficult to learn, giving far better results with ROZY feet having pleasing looks improving earning capacity for entire life, boosting psycho-physico-socio-economics of patients . Foot gets stabilized in about 6 months.
To conclude, this is the Mother of all clubfoot inventions, emanating from the earlier publications on extreme clubfoot deformities, unifying the beads in a Rosary or pearls in a necklace “Each Clubfoot is Different” is a remarkable discovery, even more is its incredible/ unsurpassed “Unity in Diversity” manifested by their treatment protocol of 4-in-1 concept. In a broader sense, it is just like: Each human being is different, yet human race is one. The Global clubfoot community in LMICs, with over 80% population, is looking towards us expectantly to fulfill their dreams.
In the texts and many parts all the 5 Figures, have been duly quoted/ printed/ adapted by kind Courtesy:
© 2020 Mittal RL. This is an open access article distributed under the terms of the Creative Commons Attribution License , which permits unrestricted use, distribution, and build upon your work non-commercially.