Case Report of an Rare Interesting Case of Golden HARS Syndrome in 3 Years Male Child

The limbal demoids in g h s are usually unilateral although they rarely can be bilateral they either involve the entire cornea or may be confined to conjunctiva only the commonest site 70 percent is infero temporal incidence is 1 in 10 000 or 1 in 500 to 2 700 they are graded according to corneal involvement grades as follows

a. Gradel is corneal epithelial involvement

b. Grade2 is des membrane involvement

c. Grade3 is entire ant segment involvement Case Report

9 months back a 3 years male child was seen by me in my office with parents having noticed a very small polish white infero temporal limbal opaciy in left eye since birth with associated cong presence of a pre auricular appendage on r side their was no other cong anamolies ft child delivered after l s c s no history of exposure to oxygen jaundice breast fed normal mile stones with normal inteligence mri orbits did not show underlying orbital involvement normal hearing a teeth and heart normal spine limbs and kidney vision ant segment refraction fundii were normal so the child had grade l l dermoid which being at the commonest site of infero temporal site[1-6].

g h s has a very good prognosis most of the children live normally with Norma vision only 5 to 15 percent may have other cong anamolies conclusion one should reassure the parent about this disorder which in majority of children is not visual threatening. However if the limbal dermoid involves visual axis and there tens vision then we have following surgical modalities as

a. Visual

b. Cosmotic

The surgical procedures are

a. Lamellar keratoplaty

b. Amionotic membrane graft

c. Stem cell graft.

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