Abstract

Angiomyolipoma (AML) is a benign mesenchymal neoplasm composed of adipose tissue, blood vessels, and smooth muscle fibres. It is most frequently located in the kidney. The second most common location of the tumor is the liver followed by the abdomen, genital organs, the heart, the mediastinum, lung, skin, head and the neck [1-4]. In the head and neck region, AML has frequently been reported to be located in the oral cavity, nasal cavity, and nasopharynx [1,2,5]. The median age of incidence is 5th decade. Accompanying tuberous sclerosis syndrome is present in 50% of angiomyolipoma patients. AML has been reported in 80% of tuberous sclerosis patients [3]. Only a few laryngeal AML cases are available in the literature [6-8].